Search on: G(M1) GANGLIOSIDE 
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Descriptor English:   G(M1) Ganglioside 
Descriptor Spanish:   Gangliósido G(M1) 
Descriptor Portuguese:   Gangliosídeo G(M1) 
Synonyms English:   Monosialosyl Tetraglycosyl Ceramide  
Tree Number:   D09.400.410.420.025.475.390
D10.390.470.025.475.390
D10.570.877.360.025.475.390
Definition English:   A specific monosialoganglioside that accumulates abnormally within the nervous system due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis. 
History Note English:   86(77); was see under GANGLIOSIDES 1977-85 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AA analogs & derivatives
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DU diagnostic use EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UR urine
Record Number:   5815 
Unique Identifier:   D005677 

Occurrence in VHL:
 

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